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Lung Development & Respiratory Physiology

How the lung is developed in utero, how breathing begins at delivery, and the physiology that sits underneath neonatal respiratory disease.

EMBRYOLOGY

How the lung develops

Lung development runs through five overlapping stages, from a small bud off the foregut to alveoli that keep multiplying for years after birth. Where development stops largely determines what is survivable - and which problems appear.

Embryonic

Weeks 4-7

The lung begins as a respiratory diverticulum (lung bud) off the ventral foregut. The trachea separates from the oesophagus and divides into the main and lobar bronchi, laying down the proximal airway template.

Clinical link: faulty tracheo-oesophageal separation underlies oesophageal atresia and tracheo-oesophageal fistula.

Pseudoglandular

Weeks 5-17

Repeated branching (branching morphogenesis) builds the conducting airways down to the terminal bronchioles. The tissue looks gland-like and no gas exchange is possible yet. The diaphragm also completes during this window.

Clinical link: failure of the pleuroperitoneal canal to close causes congenital diaphragmatic hernia; abnormal airway budding gives CPAM and sequestration.

Canalicular

Weeks 16-26

The respiratory portion forms - respiratory bronchioles and early acini. Capillaries proliferate against a thinning epithelium, and type I (gas exchange) and type II (surfactant) pneumocytes differentiate. Surfactant production begins around 24 weeks - close to the threshold of viability.

Clinical link: the lower the gestation, the thicker the air-blood barrier and the less surfactant - the core problem in extreme prematurity.

Saccular

Weeks 24-38

Terminal saccules expand the gas-exchange surface, the interstitium thins further, and surfactant rises towards maturity (around 35 weeks). Gas exchange is feasible, though reserve is limited at the earlier end.

Clinical link: surfactant deficiency through this period is the basis of respiratory distress syndrome.

Alveolar

Week 36 - childhood

True alveoli form by secondary septation. Only a fraction of the adult alveolar number is present at term; most alveoli form over the first years of life. This is why early lung injury has such lasting effects.

Clinical link: injury during active alveolarisation (ventilation, oxygen, inflammation) drives bronchopulmonary dysplasia.

KEY MOLECULES & FLUID

Surfactant and fetal lung fluid

Surfactant

Made by type II pneumocytes, surfactant is mostly phospholipid (predominantly DPPC / lecithin) plus surfactant proteins. It lowers alveolar surface tension so alveoli don't collapse at end-expiration.

By Laplace's law (P = 2T/r), a smaller alveolar radius means a higher collapsing pressure - surfactant offsets this and raises compliance. Maturity is signalled by a lecithin:sphingomyelin (L/S) ratio ≥2, and antenatal corticosteroids accelerate its production.

Full page: pulmonary surfactant →

Fetal lung fluid

The fetal lung actively secretes fluid that keeps it distended - essential for normal growth. Too little distension (oligohydramnios, large CDH) causes pulmonary hypoplasia.

Near term, labour catecholamines switch the epithelium from chloride secretion to sodium absorption (ENaC), and the lungs clear fluid. Delayed clearance - typically after caesarean without labour - produces transient tachypnoea of the newborn.

EXTRAUTERINE TRANSITION

The first breaths: four things that must happen

The fetal lung has never done gas exchange. At birth the infant must turn a fluid-filled, high-resistance organ into an air-filled one that can oxygenate and ventilate - within minutes. Four physiological events have to occur, and respiratory distress follows when any one of them fails.

Step 1

Clear the fluid

The fetal lung actively secretes chloride-rich fluid (~20-30 mL/kg by term) that is needed for lung growth and expansion. In labour, the catecholamine and cortisol surge switches the epithelium from chloride secretion to sodium (and water) absorption; the first large breaths then force remaining fluid into the interstitium, where capillaries and lymphatics clear it.

Clinical link: incomplete clearance - caesarean without labour, maternal diabetes, prematurity - causes transient tachypnoea of the newborn.

Step 2

Establish FRC

The first breath is one of the hardest efforts of life - peak pressures of 40-80 cmH₂O overcome fluid, surface tension and a compliant chest wall. Once alveoli open, surfactant lowers surface tension and later breaths are easier. Newborns defend their functional residual capacity with expiratory braking (partial glottic closure - i.e. grunting, which generates PEEP) and periodic sigh breaths - especially important in preterms.

Clinical link: too little surfactant to hold alveoli open at end-expiration → respiratory distress syndrome.

Step 3

Open the circulation

In utero, pulmonary vascular resistance is high (fluid-filled alveoli, low alveolar oxygen, vasoconstrictor mediators) and most right-ventricular output bypasses the lungs through the duct. At birth, lung inflation stretches the pulmonary vessels, the rise in PaO₂ is a potent vasodilator, and endothelial nitric oxide and prostacyclin open the circulation - pulmonary blood flow surges. Rising left atrial pressure then closes the foramen ovale, and the duct constricts over the next 24-72 hours.

Clinical link: when PVR fails to fall (meconium aspiration, sepsis, pneumonia, pulmonary hypoplasia, CDH) → persistent pulmonary hypertension.

Step 4

Keep breathing

Central chemoreceptors in the medulla respond to CO₂ and H⁺ (CO₂ crossing into CSF) - not to oxygen. Peripheral chemoreceptors in the carotid and aortic bodies give the dominant response to hypoxaemia (and also to hypercapnia and acidosis). Preterm control is immature: reduced CO₂ sensitivity, immature peripheral receptors and less stable rhythm generation.

Clinical link: immature respiratory control → apnoea of prematurity (responsive to caffeine).

If you remember only five things

  1. The fetal lung actively secretes fluid before birth.
  2. Labour hormones switch the lung from secretion to absorption.
  3. Establishing FRC is the major mechanical challenge of the first breaths.
  4. Rising oxygenation drives the postnatal fall in pulmonary vascular resistance.
  5. Apnoea of prematurity reflects immature respiratory control and reduced CO₂ responsiveness.

SUPPORTING CONCEPTS

Mechanics and gas exchange

Mechanics of ventilation

Compliance (volume change per unit pressure) is low in the surfactant-deficient and preterm lung; resistance is set by the airways. Their product is the time constant - short in RDS, so alveoli fill and empty quickly.

High surface tension and a low FRC drive a tendency to atelectasis, which is exactly why CPAP and surfactant are effective.

Gas exchange & fetal haemoglobin

Gas exchange depends on ventilation-perfusion (V/Q) matching and diffusion across the thin air-blood barrier.

Fetal haemoglobin (HbF) binds 2,3-BPG poorly, giving it a higher oxygen affinity and a left-shifted dissociation curve (lower P₅₀). This is ideal for taking up oxygen across the placenta, and is gradually replaced by adult HbA over the first months.

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